Primary Diagnosis Referral Listing
In cystic fibrosis, primary ciliary dyskinesia, or bronchiectasis, secretion clearance therapy is an established standard of care. However, in conditions other than primary disorders of the mucociliary system, Airway Clearance Therapy is generally not indicated solely on the basis of primary diagnosis; instead, prescriptions are made when an individual patient's pulmonary health is compromised by adverse events arising from one or more risk factors. The Vest® Airway Clearance System has been prescribed for airway clearance therapy for patients with respiratory complications associated with more than 600 diseases and conditions. Classifications are based on common pulmonary risk factors.
Functional Airway Deformity Disorders
- Bronchomalacia
- Bronchial Stenosis
- Castleman Disease
- Cystic Hygroma
- Esophageal Atresia
- Hypoplastic Lung
- Lung Cancer
- Malignant Pleuropulmonary Blastoma
- Tracheal-Esophageal Fistula
- Tracheal Stenosis
- Tracheomalacia
Mucociliary and Obstructive Disorders
- Alpha1-Antitrypsin Deficiency
- Asthma
- Bronchiectasis
- Bronchiolitis Obliterans
- Bronchopulmonary Dysplasia (BPD)
- Chronic Bronchitis
- Congenital Lobar Emphysema
- Cystic Fibrosis (CF)
- Emphysema
- Immotile Cilia Syndrome
- Interstitial Fibrosis
- Kartagener Syndrome
- Mucopurulent Chronic Bronchitis
- Panbronchiolitis
- Plastic Bronchitis
- Pneumoconiosis
- Primary Ciliary Dyskinesia (PCD)
- Pulmonary Alveolar Proteinosis (PAP)
- Pulmonary Papillomatosis
- Pseudohypoaldosteronism
- Right Middle Lobe Syndrome
- Smoke Inhalation
- Swyer-James-MacLeod Syndrome
- Syndrome of Inappropriate Secretion of Antidiuretic Hormone
- Yellow Nail Syndrome
Neurological/Neuromuscular Disorders
- Absent Corpus Callosum
- Acute Disseminated Encephalomyelitis
- Aicardi Syndrome
- Amyotrophic Lateral Sclerosis (ALS)
- Arnold-Chiari Malformation
- Ataxia Telangiectasia
- Brain Stem Herniation
- Canavan's Disease
- Cerebral Vascular Accident (CVA)
- Central Hypoventilation Syndrome
- Cerebral Palsy
- Congenital Cytomegalovirus (CMV)
- Congenital Hydrocephalus
- Congenital Myopathy
- Congenital Hypomyelinating Neuropathy
- Congenital Phenylketonuria
- Cerebral Atrophy
- Duchenne Muscular Dystrophy
- Epilepsy
- Familial Dysautonomia
- Fetal Varicella Syndrome
- Guillain Barre Syndrome
- Holoprosencephaly
- Hypotonia
- Idiopathic Progressive Polyneuropathy
- Krabbe's Disease
- Lennox-Gastaut Syndrome
- Leukodystrophy
- Lissencephaly
- Microcephaly
- Mitochondrial Myopathy
- Mobius Syndrome
- Moyamoya Disease
- Multiple Sclerosis
- Myasthenia Gravis
- Nemaline Myopathy
- Phrenic Nerve Paralysis
- Pompe Disease
- Post-Polio Syndrome
- Progressive Supranuclear Palsy
- Quadriplegia
- Rett Syndrome
- Richner-Hanhart Syndrome
- Severe Brain Injury
- Septo-Optic Dysplasia
- Shaken Infant Syndrome
- Shy-Drager Syndrome
- Spina Bifida
- Spinal Cord Injury
- Spinal Muscular Atrophy (SMA)
- Static Encephalopathy
- Syringomyelia
- Transverse Myelitis
- Werdnig-Hoffman Syndrome
- Williams Syndrome
Functional Airway Deformity Disorders (Genetic)
- 7Q Syndrome
- Cartilage-Hair Hypoplasia
- CHARGE Syndrome
- Down Syndrome
- Freeman-Sheldon Syndrome
- Hunter Syndrome
- Mounier-Kuhn Syndrome
- Neurofibromatosis
- Niemann-Pick Syndrome
- Opitz Syndrome
- Pierre-Robin Syndrome
- Proteus Syndrome
- Prune Belly Syndrome
- Sanfilippo Syndrome
- Trisomy 14 Q Plus
- Turner Syndrome
- VATER Syndrome
- Velo-Cardio-Facial Syndrome
Immunological Impairment Disorders
- Acquired Immune Deficiency Syndrome (AIDS-HIV)
- Acute Lymphocytic Leukemia (ALL)
- Acute Myelogenous Leukemia (AML)
- Bruton's Disease
- Chronic Granulomatosis
- Chronic Mucocutaneous Candidiasis
- Chronic Lymphocytic Leukemia (CLL)
- Chronic Myelogenous Leukemia (CML)
- Common Variable Immune Deficiency
- DiGeorge's Syndrome
- Hodgkin's Disease
- Hyperimmunoglobinemia
- Hypogammaglobulinemia
- IgA Deficiency
- Severe-Combined Immune Deficiency Syndrome (SCID)
- Sickle Cell Anemia
- Wegener's Granulomatosis
- Wiskott-Aldrich Syndrome
Primary Pulmonary Infectious Diseases
- Aspergillosis
- Atypical Mycobacterium Infection
- Mycobacterium Avium Complex (MAC)
- Pneumonia
Restrictive Lung Disorders
- Acute Respiratory Distress Syndrome (ARDS)
- Berylliosis
- Histiocytosis
- Jeune's Syndrome
- Pulmonary Fibrosis
- Rheumatoid Lung Disease
- Sarcoidosis
- Scoliosis/Kyphoscoliosis
Other
- Atrial Septal Defect (ASD)
- Cardiomyopathy
- Congestive Heart Failure
- Cushing Syndrome
- Hypoplastic Heart
- Post Organ Transplant
- Primary Pulmonary Hypertension
- Systemic Lupus Erythematosus (SLE)
- Tetralogy of Fallot
