Primary Diagnosis Referral Listing

In cystic fibrosis, primary ciliary dyskinesia, or bronchiectasis, secretion clearance therapy is an established standard of care. However, in conditions other than primary disorders of the mucociliary system, Airway Clearance Therapy is generally not indicated solely on the basis of primary diagnosis; instead, prescriptions are made when an individual patient's pulmonary health is compromised by adverse events arising from one or more risk factors. The Vest® Airway Clearance System has been prescribed for airway clearance therapy for patients with respiratory complications associated with more than 600 diseases and conditions. Classifications are based on common pulmonary risk factors.

Functional Airway Deformity Disorders

  • Bronchomalacia
  • Bronchial Stenosis
  • Castleman Disease
  • Cystic Hygroma
  • Esophageal Atresia
  • Hypoplastic Lung
  • Lung Cancer
  • Malignant Pleuropulmonary Blastoma
  • Tracheal-Esophageal Fistula
  • Tracheal Stenosis
  • Tracheomalacia

Mucociliary and Obstructive Disorders

Neurological/Neuromuscular Disorders

Functional Airway Deformity Disorders (Genetic)

  • 7Q Syndrome
  • Cartilage-Hair Hypoplasia
  • CHARGE Syndrome
  • Down Syndrome
  • Freeman-Sheldon Syndrome
  • Hunter Syndrome
  • Mounier-Kuhn Syndrome
  • Neurofibromatosis
  • Niemann-Pick Syndrome
  • Opitz Syndrome
  • Pierre-Robin Syndrome
  • Proteus Syndrome
  • Prune Belly Syndrome
  • Sanfilippo Syndrome
  • Trisomy 14 Q Plus
  • Turner Syndrome
  • VATER Syndrome
  • Velo-Cardio-Facial Syndrome

Immunological Impairment Disorders

  • Acquired Immune Deficiency Syndrome (AIDS-HIV)
  • Acute Lymphocytic Leukemia (ALL)
  • Acute Myelogenous Leukemia (AML)
  • Bruton's Disease
  • Chronic Granulomatosis
  • Chronic Mucocutaneous Candidiasis
  • Chronic Lymphocytic Leukemia (CLL)
  • Chronic Myelogenous Leukemia (CML)
  • Common Variable Immune Deficiency
  • DiGeorge's Syndrome
  • Hodgkin's Disease
  • Hyperimmunoglobinemia
  • Hypogammaglobulinemia
  • IgA Deficiency
  • Severe-Combined Immune Deficiency Syndrome (SCID)
  • Sickle Cell Anemia
  • Wegener's Granulomatosis
  • Wiskott-Aldrich Syndrome

Primary Pulmonary Infectious Diseases

  • Aspergillosis
  • Atypical Mycobacterium Infection
  • Mycobacterium Avium Complex (MAC)
  • Pneumonia

Restrictive Lung Disorders

  • Acute Respiratory Distress Syndrome (ARDS)
  • Berylliosis
  • Histiocytosis
  • Jeune's Syndrome
  • Pulmonary Fibrosis
  • Rheumatoid Lung Disease
  • Sarcoidosis
  • Scoliosis/Kyphoscoliosis

Other

  • Atrial Septal Defect (ASD)
  • Cardiomyopathy
  • Congestive Heart Failure
  • Cushing Syndrome
  • Hypoplastic Heart
  • Post Organ Transplant
  • Primary Pulmonary Hypertension
  • Systemic Lupus Erythematosus (SLE)
  • Tetralogy of Fallot